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Keratocystic odontogenic tumor related to nevoid basal cell carcinoma syndrome: clinicopathological study
Remote (Português (Brasil))

Keywords

Gorlin Syndrome
Keratocyst
Keratocystic Odontogenic Tumor
Nevoid Basal Cell Carcinoma syndrome

How to Cite

1.
Bomfin LE, Vivas APM, Rocha AC, Achatz MIW, Pinto CAL, Alves FA. Keratocystic odontogenic tumor related to nevoid basal cell carcinoma syndrome: clinicopathological study. Braz. J. Oral Sci. [Internet]. 2015 Oct. 19 [cited 2024 May 28];12(1):23-9. Available from: https://periodicos.sbu.unicamp.br/ojs/index.php/bjos/article/view/8641129

Abstract

Aim: To assess clinicopathological features of patients with keratocystic odontogenic tumor (KCOT) associated with nevoid basal cell carcinoma syndrome (NBCCS) in a single Brazilian institution. Methods: After histopathological analyses of KCOT related to NBCCS, the medical charts of 14 patients were assessed. These patients presented a total of 31 primary and 8 recurrent KCOT. Results: Out of 14 patients, 8 presented a single KCOT, 4 showed synchronous tumors, 1 had 3 metachronous lesions and another patient had 2 synchronous lesions at initial evaluation and then developed other 3 metachronous lesions. Besides the 31 primary KCOTs, 18 lesions were located in mandible and 13 in maxilla. Most tumors presented unilocular pattern and association with a tooth. Conclusions: KCOT is a frequent manifestation of NBCCS and can be its first sign, mainly in young patients. In contrast to a previously published series, most patients presented a single lesion.
Remote (Português (Brasil))
Creative Commons License

This work is licensed under a Creative Commons Attribution 4.0 International License.

Copyright (c) 2015 Luana Eschholz Bomfin, Ana Paula M. Vivas, Andre Caroli Rocha, Maria Isabel W. Achatz, Clovis Antonio L. Pinto, Fabio Abreu Alves

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