Amelogenesis imperfecta with gingival calcification: a rare presentation


  • Sunitha Carnelio Manipal College Of Dental Sciences
  • Nirmala Rao Manipal College Of Dental Sciences



Amelogenesis imperfecta. Gingival. Enamel. Hyperplasia. Calcification


The purpose of this article is to highlight the rare presence of gingival calcification with Amelogenesis Imperfecta. A case is presented of a 12-year-old girl with a defect of enamel in deciduous as well as permanent dentition with moderate amount of gingival hyperplasia with no positive family history of a similar condition. On the basis of history, clinical and radiographic features a diagnosis of autosomal recessive hypoplastic amelogenesis imperfecta of rough variant was made. Histopathological examination of hyperplastic gingival tissue revealed the presence of calcified bodies. An attempt is made to determine the nature of these calcified bodies by histochemical examination. The relevant literature is reviewed.


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Author Biography

Nirmala Rao, Manipal College Of Dental Sciences

Nirmala is Pro-Director (Learning and Teaching). She took her first degree in Economics at Delhi 
University and received her MA and MPhil from Jawaharlal Nehru University, New Delhi. She 
completed her PhD at Queen Mary and Westfield College, University of London. In 1994 she joined the 
Politics Department at Goldsmiths College where she was elected as an Academician of the Academy 
of Learned Societies in the Social Sciences in 2003. She has published extensively in the field of urban 
governance and has served as an advisor to a range of bodies including the UK Audit Commission and 
the Office of the Deputy Prime Minister (ODPM). She currently serves as a Trustee of the Learning 
from Experience Trust, and is a member of the Governing Bodies of Trinity Laban Conservatoire of Music and Dance, and the Institute of Education, University of London


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How to Cite

Carnelio S, Rao N. Amelogenesis imperfecta with gingival calcification: a rare presentation. Braz. J. Oral Sci. [Internet]. 2015 Nov. 19 [cited 2022 Nov. 26];4(15):932-5. Available from:



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